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DeCS
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Descriptor English:
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Arnold-Chiari Malformation
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Descriptor Spanish:
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Malformación de Arnold-Chiari
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Descriptor Portuguese:
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Malformação de Arnold-Chiari
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Synonyms English:
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Arnold-Chiari Deformity
Arnold-Chiari Malformation, Type 1
Arnold-Chiari Malformation, Type 2
Arnold-Chiari Malformation, Type 3
Arnold-Chiari Malformation, Type 4
Arnold-Chiari Malformation, Type I
Arnold-Chiari Malformation, Type II
Arnold-Chiari Malformation, Type III
Arnold-Chiari Malformation, Type IV
Arnold-Chiari Syndrome
Chiari Malformation Type 2
Chiari Malformation Type I
Chiari Malformation Type II
Malformation, Arnold-Chiari
Type I Arnold-Chiari Malformation
Type II Arnold-Chiari Malformation
Type III Arnold-Chiari Malformation
Type IV Arnold-Chiari Malformation
Arnold Chiari Deformity
Arnold Chiari Malformation
Arnold Chiari Malformation, Type 1
Arnold Chiari Malformation, Type 2
Arnold Chiari Malformation, Type 3
Arnold Chiari Malformation, Type 4
Arnold Chiari Malformation, Type I
Arnold Chiari Malformation, Type II
Arnold Chiari Malformation, Type III
Arnold Chiari Malformation, Type IV
Arnold Chiari Syndrome
Deformity, Arnold-Chiari
Malformation, Arnold Chiari
Syndrome, Arnold-Chiari
Type I Arnold Chiari Malformation
Type II Arnold Chiari Malformation
Type III Arnold Chiari Malformation
Type IV Arnold Chiari Malformation
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Tree Number:
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C10.500.680.291
C16.131.666.680.291
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Definition English:
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A group of congenital malformations involving the brainstem, cerebellum, upper spinal cord, and surrounding bony structures. Type II is the most common, and features compression of the medulla and cerebellar tonsils into the upper cervical spinal canal and an associated MENINGOMYELOCELE. Type I features similar, but less severe malformations and is without an associated meningomyelocele. Type III has the features of type II with an additional herniation of the entire cerebellum through the bony defect involving the foramen magnum, forming an ENCEPHALOCELE. Type IV is a form a cerebellar hypoplasia. Clinical manifestations of types I-III include TORTICOLLIS; opisthotonus; HEADACHE; VERTIGO; VOCAL CORD PARALYSIS; APNEA; NYSTAGMUS, CONGENITAL; swallowing difficulties; and ATAXIA. (From Menkes, Textbook of Child Neurology, 5th ed, p261; Davis, Textbook of Neuropathology, 2nd ed, pp236-46) |
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Indexing Annotation English:
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do not confuse with CHIARI'S SYNDROME see BUDD-CHIARI SYNDROME
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History Note English:
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2000(1963)
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Allowable Qualifiers English:
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Record Number:
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1143
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Unique Identifier:
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D001139
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Occurrence in VHL:
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Similar:
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DeCS CID-10 SciELO LILACS LIS
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